COXA VARA
Decreased Neck-Shaft Angle (less than 120°) | HE Angle is Key
CLASSIFICATION
Critical Must-Knows
- Definition: Neck-Shaft angle less than 120 degrees (Normal is 135).
- Hilgenreiner's Epiphyseal Angle (HEA): The most important prognostic factor. Normal less than 25°. greater than 60° always progresses and needs surgery.
- Biomechanics: Coxa Vara shortens the lever arm of the abductors (Trendelenburg) and increases shear stress across the physis (slip risk).
- Fairbank's Triangle: Triangular bony fragment in the inferior femoral neck metaphysis - pathognomonic for congenital coxa vara.
- Treatment: Valgus Intertrochanteric Osteotomy is the gold standard for progressive curves.
Examiner's Pearls
- "Do NOT confuse with developmental dysplasia of the hip (DDH) - in Coxa Vara the head is IN the socket.
- "Trendelenburg gait is due to mechanical disadvantage (short neck), not nerve injury.
- "HEA less than 45° usually corrects spontaneously. HEA greater than 60° basically never does.
Clinical Imaging
Imaging Gallery



Exam Differentiator
Coxa Vara vs DDH
Key Distinction: In DDH, the femoral head is subluxed/dislocated. In Congenital Coxa Vara, the head is located centrally in the acetabulum, but the NECK is deformed.
Measurement Error
Rotation Matters: Internal rotation of the leg can artificially simulate coxa valga. External rotation simulates coxa vara. Ensure standardized AP pelvis with patellae forward.
Prognostic Zones (HEA)
| HE Angle | Prognosis | Management |
|---|---|---|
| less than 45 degrees | Benzoign / Spontaneous Correction | Observation |
| 45 - 60 degrees | Indeterminate / Grey Zone | Close radiographic monitoring |
| greater than 60 degrees | Progressive / Malignant | Valgus Osteotomy |
SHORTFeatures of Congenital Coxa Vara
Memory Hook:The leg is SHORT and the abductors are weak.
PROMCauses of Acquired Coxa Vara
Memory Hook:PROM date had bad hips.
HAVSurgical Goals
Memory Hook:HAV to fix the mechanics.
Overview and Epidemiology
Coxa Vara is defined as a femoral neck-shaft angle of less than 120 degrees. It is associated with a shortened femoral neck and relative overgrowth of the greater trochanter.
Key Concepts:
- The deformity is in the NECK, not the head or shaft.
- It is a progressive dysplasia if untreated.
Epidemiology:
- Incidence: Rare (1 in 25,000 live births).
- Bilaterality: 30-50% of cases are bilateral.
- Gender: No significant gender predilection.
- Race: More common in African American population.
- Genetics: Not clearly Mendelian, but familial clustering reported (AD with incomplete penetrance).
Etiology:
- Congenital (Developmental): Primary defect in enchondral ossification of the inferior aspect of the femoral neck.
- The inferior neck fails to lengthen while the superior neck continues to grow.
- This tilts the head into varus.
- The physis becomes more vertical, subjected to shear forces (Pauwels effect), which further inhibits growth (Hueter-Volkmann law).
Pathophysiology and Mechanisms
Normal Hip
- Neck-Shaft Angle: 135 degrees (Adult), 150 degrees (Infant).
- Neck Version: 15 degrees Anteversion.
- Physis: Generally horizontal, subjected to compressive loads. Compression stimulates growth (Heuter-Volkmann).
- Abductors: Gluteus Medius inserts on GT. Distance from center of rotation (Head) to GT provides the lever arm.
Normal mechanics favor joint stability.
This relationship is crucial for gait efficiency and prevention of abductor lurch.
Classification
1. Congenital (Present at birth):
- Associated with femoral dysplasia/PFFD.
- Short femur.
2. Developmental (Infantile):
- Normal at birth.
- Presents at walking age (waddle).
- Classic type with Fairbank's triangle.
3. Acquired:
- Trauma: Physis arrest, Malunion.
- Infection: Septic hip destroying head/neck.
- Metabolic: Rickets, Renal Osteodystrophy.
- Dysplasia: Fibrous Dysplasia (Shepherd's Crook), Osteogenesis Imperfecta.
- Perthes: Sequel of head collapse.
The etiology guides the recurrence risk.
History
-
Presenting Complaint: "Painless limp".
- Age: Usually noted after walking begins (2-5 years).
- Pain: Rare in childhood. If pain is present, suspect stress fracture or superimposed pathology.
- Family History: Ask about siblings or parents (hip issues).
History of premature hip replacement in parents is a clue.
Examination
- Gait: Trendelenburg gait (lurching to affected side). If bilateral, "Waddling gait".
- Stance: Positive Trendelenburg Test.
- Leg Length: True Leg Length Discrepancy (Shortening on affected side).
- ROM:
- Abduction: Restricted (finding of impingement of GT on ilium).
- Internal Rotation: Restricted (due to retroversion).
- Flexion: Usually preserved.
- Posture: Increased lumbar lordosis (if bilateral).
Investigations
Workup Pathway
AP and Frog Leg Lateral. Measure NSA and HEA. Check for Fairbank's triangle.
If suspicion of generalized dysplasia (e.g., Cleidocranial Dysostosis, Rickets). Look for clavicle absence, widended metaphyses.
Calcium, Phosphate, ALP, Vitamin D - only if Rickets suspected.
Rarely indicated. CT may help plan 3D osteotomy for complex rotation.
Management Algorithm
Observation
- Indications:
- HEA less than 45 degrees.
- Asymptomatic.
- No progression on serial X-rays.
- Protocol: X-rays every 6-12 months.
- Outcome: The majority of curves with HEA less than 45 will spontaneously correct as the child grows.
Shoe lifts can be used for leg length discrepancy but do not correct the deformity.
Surgical Technique
Approach Warning
Vascular Safety: The medial circumflex femoral artery (MCFA) is at risk during posterior approaches or aggressive medial dissection. The lateral approach is safer but requires deeper retraction. Avoid damaging the trochanteric apophysis in young children (less than 5 years) to prevent iatrogenic growth arrest.
Valgus Intertrochanteric Osteotomy
Principle: A closing wedge valgus osteotomy (remove lateral wedge) or opening wedge medial. Closing wedge is safer for union.
Steps:
- Setup: Supine on radiolucent table. Fluoroscopy.
- Approach: Direct lateral approach to proximal femur. Elevate Vastus Lateralis.
- Careful hemostasis of perforating vessels.
- Expose the flare of the greater trochanter.
- Guide Wire: Insert guide wire into femoral neck/head.
- The angle of insertion determines correction.
- If using a 130 deg blade plate, insert wire at predetermined angle to shaft to achieve desired valgus.
- Seating Chisel: Insert seating chisel over/parallel to wire.
- Osteotomy:
- Perform intertrochanteric bone cut.
- Remove a laterally based wedge of bone (calculated from preoperative tracing).
- Tip: The size of the wedge (in mm) roughly equals the degrees of correction needed on some plating systems, but templates are safer.
- Reduction: Abduct the shaft to close the osteotomy. The head/neck unit is now more valgus.
- Fixation: Insert Blade Plate or Pediatric Locking Plate (cannulated screw system).
- Rotation: Correct retroversion by internally rotating the distal fragment before plating (if needed).
- Adductor Tenotomy: Often required (percutaneous) as valgus lengthens the leg and tightens adductors.
Post-Op: Spica cast usually needed for younger children (less than 6-8). Protected weight bearing for older.
Pitfalls to Avoid:
- Under-correction (High recurrence rate).
- Anterior penetration of the plate (femoral neck is retroverted).
- Injury to the trochanteric apophysis (posterior approach).
Careful preoperative planning is the key to avoiding these pitfalls.
Complications
| Complication | Risk Factor | Prevention | Management |
|---|---|---|---|
| Recurrence | Under-correction (HEA greater than 35) | Overcorrect to valgus | Repeat Osteotomy |
| Physeal Closure | Surgical trauma to physis | Stay 1cm from physis | Epiphysiodesis contralateral |
| AVN | Vessel injury | Careful dissection | Bisphosphonates / Salvage |
| Malunion | Loss of fixation | Spica cast augmentation | Osteotomy |
| Leg Length Discrepancy | Unilateral disease | Shoe lifts | Contralateral Epiphysiodesis |
| Infection | Surgeon error | Antibiotics | Washout |
Premature closure of the capital femoral physis is a devastating complication. It leads to a short femoral neck (Coxa Breva) and recurrence of varus if the troch continues to grow. It usually results from direct surgical trauma (drill/chisel) or vascular injury.
Recurrence Rule
The most common cause of recurrence is under-correction. If the HEA is not restored to less than 40 degrees (ideally less than 30), the shear forces remain, and the deformity will recur via the Hueter-Volkmann principle.
Postoperative Care
Protocol:
- Immobilization:
- Age less than 6-8 years: Hip Spica Cast for 6 weeks. Fixation alone is often insufficient for active children.
- Age greater than 8 years: Touch weight bearing with crutches (if reliable).
- X-rays:
- Check at 6 weeks for union.
- Check at 3 months, 6 months, 1 year.
- Hardware Removal:
- Often required once healed (12-18 months) as the plate will become buried in bone and hard to remove later.
- Blade plates can act as stress risers.
Rehab Phase 1 (0-6 weeks):
- Spica cast or Non-weight bearing.
- Ensure cast comfort.
- Monitor for cast sores.
Rehab Phase 2 (6-12 weeks):
- Cast removal.
- X-ray to confirm union.
- Hydrotherapy / Pool walking.
- Gentle active ROM (Abduction/Flexion).
- Touch weight bearing.
Rehab Phase 3 (3-6 months):
- Full weight bearing.
- Abductor strengthening (Clamshells).
- Normalise gait.
- Monitor for leg length discrepancy.
Outcomes and Prognosis
- Natural History:
- HEA less than 45: 80% spontaneous resolution.
- HEA greater than 60: 100% progression. untreated leads to severe shortening, limp, and early OA.
- Surgical Outcomes:
- Success Rate: 90% correction if adequate valgus achieved.
- Limp: Usually resolves if biomechanics are restored.
- Leg Length: Osteotomy lengthens the leg (valgus gain), but pre-existing physeal arrest may result in permanent shortening (0.5 - 2 cm).
- Long Term:
- Even with correction, the hip is rarely "normal".
- Acetabular dysplasia usually remodels if head is centered.
- Mild risk of OA remains.
Evidence Base
HEA Prognostic Value
- Classic study defining HE Angle utility
- HEA less than 45 degrees: Observation correct
- HEA greater than 60 degrees: Surgery mandatory
- HEA 45-60: Grey zone, follow closely
Valgus Osteotomy Outcomes
- Review of 20 hips treated with Valgus Osteotomy
- Recurrence rate correlated with post-op HEA
- Correction of HEA directly determined outcome
- Recommended overcorrection to 140-150 degrees NSA
Blade Plate vs Locking Plate
- Comparison of fixation methods
- Blade plates provided rigid fixation but technically demanding
- Locking plates easier to apply but expensive
- Union rates similar
Genetics of Coxa Vara
- Review of familial cases
- Pattern suggests AD inheritance with variable penetrance
- Associated with Cleidocranial Dysostosis
- Screen parents/siblings
Recurrence Mechanisms
- Biomechanical analysis of varus hip
- Defined shear vs compression forces on physis
- Calculated that HEA greater than 30 introduces shear
- Foundation of osteotomy planning
Exam Viva Scenarios
Practice these scenarios to excel in your viva examination
Scenario 1: The Waddling Toddler
"A 3-year-old is brought in by parents for a waddling gait. Painless. Unremarkable birth history. Describe your assessment."
Scenario 2: The Grey Zone
"You see a 4-year-old with bilateral Coxa Vara. HE Angle is 50 degrees on the right and 55 on the left. Parents are worried. Plan?"
Scenario 3: Post-Op Recurrence
"You performed a osteotomy 1 year ago. X-rays now show the varus has returned. What happened and what now?"
Scenario 4: The 10 Year Old
"A 10-year-old presents with neglected coxa vara. Short leg (-3cm). HEA 70 degrees. Is it too late?"
Scenario 5: The Adult Sequelae
"A 30-year-old presents with unilateral hip pain. X-rays show a pistol-grip deformity and mild OA. History of childhood osteotomy. What is this?"
MCQ Practice Points
Question 1
Q: The most reliable radiographic measurement for predicting progression in Congenital Coxa Vara is: A. Neck-Shaft Angle B. Hilgenreiner's Epiphyseal Angle (HEA) C. Acetabular Index D. Articulo-trochanteric distance Answer: B. The HEA measures the obliquity of the physis. A vertical physis (greater than 60 deg) predicts progression due to shear.
Question 2
Q: Which feature distinguishes Congenital Coxa Vara from Developmental Dysplasia of the Hip (DDH)? A. Short leg B. Trendelenburg gait C. Head located in acetabulum D. Limited abduction Answer: C. In DDH, the head is subluxed/dislocated. In Coxa Vara, the head is reduced, but the neck is bent.
Question 3
Q: An HE Angle of 70 degrees is an indication for: A. Observation B. Shoe lift C. Valgus Osteotomy D. Arthrodesis Answer: C. HEA greater than 60 degrees is the absolute indication for surgery as spontaneous resolution does not occur.
Question 4
Q: Fairbank's triangle represents: A. A fracture B. A defect in ossification C. A tumor D. Infection Answer: B. It is a triangular cartilaginous defect in the inferior femoral neck ossification center.
Question 5
Q: The primary biomechanical goal of osteotomy in Coxa Vara is to: A. Lengthen the leg B. Convert shear forces to compression C. Improve cosmesis D. Reduce the head Answer: B. By making the physis horizontal (HEA less than 30), shear forces (which inhibit growth) are converted to extensive/compressive forces (which stimulate growth).
Australian Context
Epidemiology:
- Rarer in Australia than DDH.
- Often presents late in rural communities as "waddle".
Implants:
- Synthes Pediatric Locking Hip Plates (LCP) are the standard in most pediatric centers (Children's Hospitals).
- Blade plates (fixed angle) are classic but technically less forgiving.
Referral Pathways:
- HEA less than 45: General Ortho/Paeds can monitor.
- HEA greater than 45 or Surgery: Refer to Tertiary Pediatric Orthopaedic Unit (RCH, SCH, QCH etc) for osteotomy. Complex multi-planar corrections needed.
Medicare:
- Specific funding exists for femoral osteotomy.
- If bilateral, staged procedures usually preferred to allow for rehabilitation between sides.
- Public hospital waiting lists for "non-urgent" deformity correction can be long.
Coxa Vara Essentials
High-Yield Exam Summary
Key Numbers
- •Normal NSA: 135 deg
- •Coxa Vara: less than 120 deg
- •Severe Vara: less than 90 deg
- •Normal HEA: less than 25 deg
- •Surgery Indicator: HEA greater than 60 deg
- •Grey Zone: 45-60 deg
Pathology
- •Vertical Physis
- •Ossification defect (Fairbank's Triangle)
- •Shear forces inhibit growth
- •Short neck + High Trochanter
Clinical
- •Painless limp
- •Trendelenburg Gait
- •Short leg
- •Limited Abduction/Int Rotation
Surgery
- •Valgus Intertrochanteric Osteotomy
- •Adductor Tenotomy
- •Spica Cast (if young)
- •Overcorrect (Valgus is good)